INTRODUCTION: Twin pregnancy is defined as one that originates from one or more ovulatory cycles, resulting in the intrauterine development of more than one zygote or the division of the same zygote, regardless of the final number of neonates. It is associated with a high risk of perinatal mortality and may be dizygotic or monozygotic. OBJECTIVES: To report a case of monochorionic and monoamniotic twin pregnancy in a patient attended at Ary Pinheiro Base Hospital (HBAP) and review literature on this subject. METHODOLOGY: The present study uses a bibliographical research reference, in order to obtain information and report on the case of monochorionic and monoamniotic twin pregnancy in a patient attended at Ary Pinheiro Base Hospital (HBAP) Porto Velho - RO. CASE REPORT: Patient EO, female, 26 years old, white, catholic, married, household, G1P0A0, GI 32 weeks (USG of 6s + 2d), is referred from Ariquemes - RO, by monochorionic gemelarity And monoamniotic, diagnosed in USG at 13 weeks. No other complaints. At the entrance exam, AFU: 35cm; MF: present; DU: absent, normal uterine tone and absence of metrossystoles. BCF fetus (1): 144bpm / BCF fetus (2): 150bpm. Specular: Centralized colon, well epithelized, punctate orifice, without apparent lesions. Vaginal Touch: Thick, posterior, impromptu neck. USG with 6 weeks and 2 days and another with 12 weeks and 5 days lauded with Monoamniotic and monochorionic gestation. Conduct: Obstetric Doppler every two days; Corticoid for pulmonary maturation; BCF 3x / day; Mobilogram and Gestation Resolution with 34 weeks if available vacant in pediatric ICU. Gestation was discontinued at 35 days of age + 6 days, without intercurrences and without need for ICU admission.